Vol. 25 No. 2 (2021)
CASE REPORTS

Case report: Implantation of a personal aortic corset to stabilize the size of the root and the ascending aorta in a patient with Marfan syndrome

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  • A.S. Nesmachnyy,
  • A.M. Chernyavskiy,
  • Yu.E. Kareva
A.S. Nesmachnyy
Meshalkin National Medical Research Center, Novosibirsk
Bio
A.M. Chernyavskiy
Meshalkin National Medical Research Center, Novosibirsk
Yu.E. Kareva
Meshalkin National Medical Research Center, Novosibirsk
DOI: https://doi.org/10.21688/1681-3472-2021-2-87-94

Published 2021-06-28

Keywords

  • aneurysm of ascending aorta,
  • aortic exoprosthetics,
  • epiaortic wrapping,
  • case report,
  • Marfan syndrome,
  • personal aortic corset
    • ...More
    Less

How to Cite

Nesmachnyy, A., Chernyavskiy, A., & Kareva, Y. (2021). Case report: Implantation of a personal aortic corset to stabilize the size of the root and the ascending aorta in a patient with Marfan syndrome. Patologiya Krovoobrashcheniya I Kardiokhirurgiya, 25(2), 87–94. https://doi.org/10.21688/1681-3472-2021-2-87-94

Copyright (c) 2021 Nesmachnyy A.S., Chernyavskiy A.M., Kareva Yu.E.

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

Abstract

Herein, we report a case of a patient with Marfan syndrome for whom we successfully stabilized the root and the ascending aorta to prevent further expansion and reduce the aortic rupture risk. For stabilization, a personal aortic corset was used, cut, and formed as per the individual anatomical parameters of the patient (external dimensions of the root and the ascending aorta). Using a personalized approach, we could create a stabilizing aortic framework that matched the anatomical dimensions of the root and the ascending aorta of the patient. Implantation of a personal aortic corset with borderline dimensions of the root and the ascending aorta enabled us to prevent major surgical trauma, artificial circulation, and postoperative anticoagulant therapy as well as lower the risk of further expansion and aorta rupture in our patient, who was predisposed to these events. Postoperative results 1 year later showed the absence of negative dynamics regarding an increase in the size of the root and the ascending aorta or hemodynamic disorders in the aortic valve of our patient with Marfan syndrome.

Received 29 January 2021. Revised 15 March 2021. Accepted 16 March 2021.

Funding: The study did not have sponsorship.

Conflict of interest: Authors declare no conflict of interest.

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