Vol. 24 No. 2 (2020)
CASE REPORTS

Undifferentiated pleomorphic sarcoma of the right atrium in an infant

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  • I. Murashov,
  • V. Kliver,
  • T. Ageeva,
  • A. Volkov,
  • E. Kliver
I. Murashov
Meshalkin National Medical Research Center, Novosibirsk
Bio
V. Kliver
Novosibirsk State Medical University, Novosibirsk
T. Ageeva
Novosibirsk State Medical University, Novosibirsk
A. Volkov
Meshalkin National Medical Research Center, Novosibirsk
E. Kliver
Meshalkin National Medical Research Center, Novosibirsk
DOI: https://doi.org/10.21688/1681-3472-2020-2-119-123

Published 2020-07-03

Keywords

  • cardiac sarcoma,
  • сase report,
  • primary cardiac sarcoma,
  • undifferentiated pleomorphic sarcoma

How to Cite

Murashov, I., Kliver, V., Ageeva, T., Volkov, A., & Kliver, E. (2020). Undifferentiated pleomorphic sarcoma of the right atrium in an infant. Patologiya Krovoobrashcheniya I Kardiokhirurgiya, 24(2), 119–123. https://doi.org/10.21688/1681-3472-2020-2-119-123

Copyright (c) 2020 Murashov I.S., Kliver V.E., Ageeva T.A., Volkov A.M., Kliver E.E.

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

Abstract

Undifferentiated pleomorphic sarcoma is a high-grade malignant tumour, accounting for one-third of all primary cardiac sarcomas. This paper describes a case of undifferentiated pleomorphic sarcoma in an infant using detailed morphological characterisation, immunohistochemical examination and a brief literature review. Taken together, these data will be useful not only for practicing pathologists but also for researchers of other biomedical fields for the development of procedures for differential diagnoses, investigation of the pathogenesis and development of therapeutic approaches for undifferentiated pleomorphic sarcoma.

Received 4 February 2019. Revised 31 March 2020. Accepted 9 April 2020.

Funding: The study did not have sponsorship.

Conflict of interest: Authors declare no conflict of interest.

Author contributions
Drafting the article: I.S. Murashov, E.E. Kliver
Literature review: V.E. Kliver, T.A. Ageeva
Illustrations: V.E. Kliver, A.M. Volkov
Critical revision of the article: I.S. Murashov, E.E. Kliver
Final approval of the version to be published: I.S. Murashov, V.E. Kliver, T.A. Ageeva, A.M. Volkov, E.E. Kliver

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