Vol. 24 No. 2 (2020)
CASE REPORTS

A clinical case of repeated correction of Ebstein’s anomaly using the ‘cone reconstruction’ method

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  • N. Troshkinev,
  • E. Svyazov,
  • O. Mochula,
  • N. Shmakova,
  • I. Ivanova,
  • O. Egunov,
  • E. Krivoshchekov
N. Troshkinev
Cardiology Research lnstitute, Tomsk National Research Medical Center, Russian Academy of Sciences, Tomsk
Bio
E. Svyazov
Cardiology Research lnstitute, Tomsk National Research Medical Center, Russian Academy of Sciences, Tomsk
O. Mochula
Cardiology Research lnstitute, Tomsk National Research Medical Center, Russian Academy of Sciences, Tomsk
N. Shmakova
Cardiology Research lnstitute, Tomsk National Research Medical Center, Russian Academy of Sciences, Tomsk
I. Ivanova
Cardiology Research lnstitute, Tomsk National Research Medical Center, Russian Academy of Sciences, Tomsk
O. Egunov
Cardiology Research lnstitute, Tomsk National Research Medical Center, Russian Academy of Sciences, Tomsk
E. Krivoshchekov
Cardiology Research lnstitute, Tomsk National Research Medical Center, Russian Academy of Sciences, Tomsk
DOI: https://doi.org/10.21688/1681-3472-2020-2-102-108

Published 2020-07-03

Keywords

  • case report,
  • congenital heart disease,
  • cone reconstruction,
  • Ebstein’s anomaly,
  • repeated surgery

How to Cite

Troshkinev, N., Svyazov, E., Mochula, O., Shmakova, N., Ivanova, I., Egunov, O., & Krivoshchekov, E. (2020). A clinical case of repeated correction of Ebstein’s anomaly using the ‘cone reconstruction’ method. Patologiya Krovoobrashcheniya I Kardiokhirurgiya, 24(2), 102–108. https://doi.org/10.21688/1681-3472-2020-2-102-108

Copyright (c) 2020 Troshkinev N.M., Svyazov E.A., Mochula O.V., Shmakova N.A., Ivanova I.V., Egunov O.A., Krivoshchekov E.V.

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

Abstract

We report the case of a 16-year-old child with Ebstein’s anomaly who successfully underwent recorrection via the ‘cone reconstruction’ method using a tricuspid valve-in-ring implant. Because the patient had high-grade atrioventricular block, a pacemaker was implanted. Ultrasound and magnetic resonance imaging were conducted to determine the anatomy of the right ventricle and its hemodynamic parameters. Echocardiography performed at the time of discharge revealed an improvement in the hemodynamic parameters of the patient after the correction: triuspid valve regurgitation is mild and peak/mean pressure gradient 10/5 mmHg.

Received 9 January 2020. Revised 16 March 2020. Accepted 17 March 2020.

Informed consent: The patient’s informed consent to use the records for medical purposes is obtained.

Funding: The study did not have sponsorship.

Conflict of interest: Authors declare no conflict of interest.

Author contributions
Drafting the article: N.M. Troshkinev, O.V. Mochula, O.A. Egunov
Literature review: N.A. Shmakova, I.V. Ivanova
Illustrations: N.M. Troshkinev, O.V. Mochula
Critical revision of the article: E.V. Krivoshchekov, E.A. Svyazov
Surgical treatment: E.V. Krivoshchekov, O.A. Egunov, N.M. Troshkinev
Final approval of the version to be published: N.M. Troshkinev, E.A. Svyazov, O.V. Mochula, N.A. Shmakova, I.V. Ivanova, O.A. Egunov, E.V. Krivoshchekov

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