Vol. 22 No. 1 (2018)
CASE REPORTS

Valve-sparing aneurysmal root/ascending aorta replacement in a 9-year-old patient with Marfan syndrome

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  • V. Bogdanov,
  • I. Gladyshev,
  • E. Kharisova,
  • I. Harenko
V. Bogdanov
Federal Center of Cardiovascular Surgery (Chelyabinsk), Ministry of Health of Russian Federation, Chelyabinsk, Russian Federation
I. Gladyshev
Federal Center of Cardiovascular Surgery (Chelyabinsk), Ministry of Health of Russian Federation, Chelyabinsk, Russian Federation
E. Kharisova
Federal Center of Cardiovascular Surgery (Chelyabinsk), Ministry of Health of Russian Federation, Chelyabinsk, Russian Federation
Bio
I. Harenko
Federal Center of Cardiovascular Surgery (Chelyabinsk), Ministry of Health of Russian Federation, Chelyabinsk, Russian Federation
DOI: https://doi.org/10.21688/1681-3472-2018-1-61-65

Published 2018-04-02

Keywords

  • valve-sparing surgery,
  • David procedure,
  • connective tissue dysplasia

How to Cite

Bogdanov, V., Gladyshev, I., Kharisova, E., & Harenko, I. (2018). Valve-sparing aneurysmal root/ascending aorta replacement in a 9-year-old patient with Marfan syndrome. Patologiya Krovoobrashcheniya I Kardiokhirurgiya, 22(1), 61–65. https://doi.org/10.21688/1681-3472-2018-1-61-65

Copyright (c) 2018 Bogdanov V.N., Gladyshev I.V., Kharisova E.F., Harenko I.V.

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

Abstract

A clinical case report of a 9-year-old patient with a severe form of Marfan syndrome and significant enlargement of the aortic root and mitral/tricuspid valve failure is presented. The patient underwent successful one-stage surgical repair including reimplantation of the aortic valve using David procedure, mitral valve annuloplication and De Vega valvuloplasty of the tricuspid valve.

Received 21 November 2017. Revised 19 February 2018. Accepted 27 February 2018.

Funding: The study did not have sponsorship.

Conflict of interest: Authors declare no conflict of interest.

Author contributions
All authors contributed equally to the work.

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References

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