Vol. 20 No. 3 (2016)
CASE REPORTS

A case of “non-compact myocardium” cardiomyopathy diagnosed and treated by means of implantable cardioverter-defibrillators

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  • I Dorovskikh,
  • Yu Vakhnenko,
  • V Shabanov,
  • E Gordienko,
  • A Verevetinov
I Dorovskikh
Amur State Medical Academy, Ministry of Health Care of Russian Federation, 675006 Blagoveshchensk, Amur Region, Russian Federation
Bio
Yu Vakhnenko
Amur State Medical Academy, Ministry of Health Care of Russian Federation, 675006 Blagoveshchensk, Amur Region, Russian Federation
V Shabanov
Research Institute of Circulation Pathology, 630055 Novosibirsk, Russian Federation
E Gordienko
Amur State Medical Academy, Ministry of Health Care of Russian Federation, 675006 Blagoveshchensk, Amur Region, Russian Federation
A Verevetinov
Amur State Medical Academy, Ministry of Health Care of Russian Federation, 675006 Blagoveshchensk, Amur Region, Russian Federation
DOI: https://doi.org/10.21688/1681-3472-2016-3-126-131

Published 2016-11-10

Keywords

  • cardiomyopathy,
  • “non-compact" myocardium,
  • cardioverter defibrillator

How to Cite

Dorovskikh, I., Vakhnenko, Y., Shabanov, V., Gordienko, E., & Verevetinov, A. (2016). A case of “non-compact myocardium” cardiomyopathy diagnosed and treated by means of implantable cardioverter-defibrillators. Patologiya Krovoobrashcheniya I Kardiokhirurgiya, 20(3), 126–131. https://doi.org/10.21688/1681-3472-2016-3-126-131

Copyright (c) 2016 Dorovskikh I.E., Vakhnenko Yu.V., Shabanov V.V., Gordienko E.N., Verevetinov A.N.

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

Abstract

The article presents a case of non-compact myocardium primary diagnosis of a woman of 45 years, who has complained of general weakness, pain in the heart and interruptions in its work, shortness of breath and dizziness from her youth. A peculiarity of this case is that the patient was initially examined locally and diagnosed with rheumatic heart disease and then with ischemic heart disease. However, the age at which the disease made its debut, the characteristics of pain in the heart, the severity of symptoms of arrhythmia and heart failure, no changes of blood lipid spectrum and other signs of atherosclerosis raised doubts about the presence of angina. Since the clinical syndromes showed a marked violation of all basic functions of the heart muscle, differential diagnostics with diffuse myocarditis was performed, which led to the latter’s exclusion. During ECHO CT followed by transesophageal ECHO at the Academy’s Cardiac Surgery Department, primary “non-compact myocardium” cardiomyopathy was diagnosed. Provided the patient’s complex arrhythmias, a cardioverter-defibrillator with a pacemaker function was implanted and her health significantly improved.

Received 9 August 2016. Accepted 28 September 2016.

Funding: The study has not been sponsored or awarded a grant.
Conflict of interest:The authors declare no conflict of interest.

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